Budd-Chiari Syndrome
ثبت نشده
چکیده
Budd-Chiari syndrome (BCS) is a rare condition which occurs when there is obstruction of the hepatic veins. It includes any condition in which there is obstruction to venous flow from the small hepatic veins to the inferior vena cava. It should be differentiated from veno-occlusive disease in which the sinusoidal epithelial cells of the hepatic venules are damaged; this mainly occurs after stem-cell transplantation.
منابع مشابه
A Rare Case of Budd Chiari Syndrome in a Child
A 7-year- old male child presented with the complaints of tense abdominal distension and swelling over feet since 1 month. The patient had repeated episodes of similar complaints since last two years with partial or complete relief after taking various forms of allopathic therapy. On imaging, Budd-Chiari syndrome was diagnosed which was hallmarked by occluded Inferior venacava (IVC), caudate lo...
متن کاملBudd-Chiari Syndrome Caused by TIPS Malposition: A Case Report
Budd-Chiari syndrome refers to hepatic pathology secondary to diminished venous outflow, most commonly associated with venothrombotic disease. Clinically, patients with Budd-Chiari present with hepatomegaly, ascites, abdominal distension, and pain. On imaging, Budd-Chiari syndrome is hallmarked by occluded IVC and or hepatic veins, caudate lobe enlargement, heterogeneous liver enhancement, intr...
متن کاملThe Long-Term Outcomes for Patients with Budd-Chiari Syndrome Caused by Behcet’s Disease: A Case Series on the Results, from Cirrhosis to Death
BACKGROUND Budd-Chiari syndrome, which is a rare complication of Behcet's disease, carries a high mortality rate. OBJECTIVES The aim of the study was to present our long-term follow up experience with patients suffering from Budd-Chiari syndrome due to Behcet's disease. METHODS The records of 402 patients with Behcet's disease were evaluated retrospectively. To facilitate detection of the l...
متن کاملBudd-Chiari syndrome in association with Behçet's disease: review of the literature.
The risk that patients with Behçet's disease may develop various thrombotic complications has been previously described. Although vascular complications from Budd-Chiari syndrome associated with Behçet's disease have been described, the pathogenic mechanisms are still unknown. Severe vascular complications present in Budd-Chiari syndrome associated with Behçet's disease are very common among yo...
متن کامل[Budd-Chiari syndrome].
The budd-Chiari syndrome is characterized by thrombotic or non thrombotic reduction of the venous hepatic flow. Several works have enabled the comprehension of budd-Chiari syndrome as well as the diagnosis and treatment. This clinical review attempted to present the budd-Chiari syndrome overall and more particularly the history, etiology, pathophysiology, diagnosis and the understanding of the ...
متن کاملRuptured Hepatocellular Carcinoma in a Child with Budd-Chiari Syndrome.
BACKGROUND Hepatocellular carcinoma is an uncommon complication described in patients with Budd-Chiari syndrome. CASE CHARACTERISTICS A 12-year-old boy with Budd-Chiari syndrome, who was earlier treated with Transjugular intrahepatic porto-systemic shunt (TIPS), presented with acute onset hemoperitoneum and hypotension. OUTCOME It was diagnosed to be a case of ruptured hepatocellular carcin...
متن کامل